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Oct 14, 2011 · Abstract. Binder syndrome or maxillonasal dysplasia is an uncommon developmental anomaly affecting primarily the anterior part of the maxilla and nasal complex. The characteristic findings are a failure of development in the premaxillary area with associated deformities of the nasal skeleton and the overlying soft tissues. Affected individuals ...
- Upendra Jain, Gagan Thakur, Amitabh Kallury
- 10.1136/bcr.08.2011.4665
- 2011
- BMJ Case Rep. 2011; 2011: bcr0820114665.
Apr 27, 2020 · The exact cause of Binder syndrome is not fully understood. Most cases appear to occur sporadically, but familial cases have been reported as well. Surgical and orthodontic treatment is recommended. Introduction. Binder type nasomaxillary dysplasia was first described in the medical literature as far back 1882. Dr.
- Causes and Symptoms of Binder Syndrome
- Epidemiology of Binder Syndrome
- Association with Chondrodysplasia punctata
- Diagnosis and Treatment of Binder Syndrome
- References
- Further Reading
Binder syndrome is a type of condition that can emerge on its own. The majority of occurrences, however, are linked to genetic diseases such the Xp22.3 deletion and cholesterol problems. This syndrome is also linked to vitamin K insufficiency and alloimmune maternal illnesses, including systemic lupus erythematosus. Reports link Binder's syndrome t...
Binder's syndrome affects both men and women equally. The syndrome is uncommon, which may explain why little is known about its underlying genesis, inheritance patterns, and genuine prevalence.
The prevalence of Binder syndrome is unknown since it is frequently misdiagnosed as X-linked chondrodysplasia punctata due to comparable facial deformities. A deficit of the Golgi enzyme ARSE, whose gene is found in Xp22.3, causes X-linked chondrodysplasia punctata, a congenital condition of bone and cartilage growth. Pneumonia, cervical spine comp...
Similar facial features in other syndromes, such as Warfarin embryopathy, Down syndrome, Apert syndrome, and others, are used to make the differential diagnosis for Binder's syndrome. During fetal ultrasonogram (USG) exams, these syndromes are frequently misdiagnosed. Beginning in the 21st week of pregnancy, Binder's syndrome can be easily detected...
Gupta, A., Aneja, A., Bahl, N. et al. (2021). Prenatal Binder Phenotype: Physician's Dilemma-A Case Report. J. Fetal Med. 8, 65–70. https://doi.org/10.1007/s40556-020-00283-2Blask, A. R., Rubio, E. I., Chapman, K. A., Lawrence, A. K., & Bulas, D. I. (2018). Severe nasomaxillary hypoplasia (Binder phenotype) on prenatal US/MRI: an important marker for the prenatal diagn...Araujo Júnior E., Tonni G., Sepulveda W. (2017). Binder Syndrome: Prenatal Diagnosis, Management, and Prognosis. In: Tonni G., Sepulveda W., Wong A. (eds) Prenatal Diagnosis of Orofacial Malformati...Venkatesh A, Anuradha B, Karthick A, Mouli P. E. C, Ramasamy M. (2016). Binder's Syndrome – A Rare Case Report and Review of Literature with Detailed Treatment Plan. Biomed Pharmacol J. 9(3).Binder syndrome is a rare congenital (present-at-birth) condition. The main symptom is underdevelopment in the central part of your face. People with the condition may have an unusually flat nose or a lower jaw that sticks out farther than usual. In most people, orthodontic care and plastic surgery successfully treat the condition.
Some authors consider maxillonasal dysplasia as an allelic form of chondrodysplasia punctata. Others suggest that it does not represent a distinct disease entity or syndrome, but rather is a nonspecific abnormality of the nasomaxillary regions. Holoproencephaly and arhinencephaly are the two main differential diagnosis, but there is no brain ...
Jan 29, 2014 · Introduction. Invasive fungal infections caused by the members of Mucorales (mucormycosis) are relatively rare but have increased in the last years 1.These aggressive and highly destructive infections occur predominantly in immunocompromised hosts, especially in patients with haematological malignancies or those receiving hematopoietic stem cell transplantation.
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What is Binder Syndrome (Binder type Nasomaxillary dysplasia)?
Binder syndrome is a problem of part of the nose and upper jaw. Affected individuals have a very flat nose and an underdeveloped upper jaw. The characteristics of the syndrome are typically visible when looking at the profile of the face. The profile looks flat with a relatively protruding lower jaw. The facial anomalies in Binder syndrome may ...
